| 别名 | Peroxin 26, Peroxisome assembly protein 26, PEX26, PEX26M1T, Pex26pM1T |
| 产品类型 | Polyclonal |
| 基因名称 | peroxisomal biogenesis factor 26 |
| 经测试应用 | WB |
| 宿主 | Rabbit |
| 种属反应性 | Human |
| 免疫原 | A synthesized peptide derived from human PEX26 |
| 理论分子量 | 34 kDa |
| 实际分子量 | 34 kDa |
| Gene ID(NCBI) | 55670 |
| GeneBank Accession Number | BC016280 |
| UNIPROT | Q7Z412 |
| 形式 | Liquid |
| 保存条件 | Store at -20℃. Stable for one year after shipment. Aliquoting is unnecessary for -20℃ storage. |
| 推荐稀释比例 | 1:500-1:2000 |
| 背景信息 | This gene belongs to the peroxin-26 gene family. It is probably required for protein import into peroxisomes. It anchors PEX1 and PEX6 to peroxisome membranes, possibly to form heteromeric AAA ATPase complexes required for the import of proteins into peroxisomes. Defects in this gene are the cause of peroxisome biogenesis disorder complementation group 8 (PBD-CG8). PBD refers to a group of peroxisomal disorders arising from a failure of protein import into the peroxisomal membrane or matrix. The PBD group is comprised of four disorders: Zellweger syndrome (ZWS), neonatal adrenoleukodystrophy (NALD), infantile Refsum disease (IRD), and classical rhizomelic chondrodysplasia punctata (RCDP). Alternatively spliced transcript variants have been identified for this gene. |